Composite pheochromocytoma with a malignant peripheral nerve sheath tumor: Case report and review of the literature

被引：10

作者：

Namekawa, Takeshi ^{[1
]}

Utsumi, Takanobu ^{[1
]}

Imamoto, Takashi ^{[1
]}

Kawamura, Koji ^{[1
]}

Oide, Takashi ^{[2
]}

Tanaka, Tomoaki ^{[3
]}

Nihei, Naoki ^{[1
]}

Suzuki, Hiroyoshi ^{[4
]}

Nakatani, Yukio

Ichikawa, Tomohiko ^{[1
]}

机构：

[1] Chiba Univ, Grad Sch Med, Dept Urol, Chiba, Japan

[2] Chiba Univ, Grad Sch Med, Dept Diagnost Pathol, Chiba, Japan

[3] Chiba Univ, Grad Sch Med, Dept Clin Cell Biol, Chiba, Japan

[4] Toho Univ, Sakura Med Ctr, Dept Urol, Sakura, Japan

来源：

ASIAN JOURNAL OF SURGERY | 2016年 / 39卷 / 03期

关键词：

adrenalectomy; adrenal tumor; malignant peripheral nerve sheath tumor; pheochromocytoma; spontaneous rupture; SPONTANEOUS RUPTURE; DISEASE;

D O I：

10.1016/j.asjsur.2012.11.003

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Adrenal tumors with more than one cellular component are uncommon. Furthermore, an adrenal tumor composed of a pheochromocytoma and a malignant peripheral nerve sheath tumor is extremely rare. A composite pheochromocytoma with malignant peripheral nerve sheath tumor in a 42-year-old man is reported here. After adequate preoperative control, left adrenalectomy was performed simultaneously with resection of the ipsilateral kidney for spontaneous rupture of the left adrenal tumor. Pathological findings demonstrated pheochromocytoma and malignant peripheral nerve sheath tumor in a ruptured adrenal tumor. To date, there have been only four reported cases of composite pheochromocytoma with malignant peripheral nerve sheath tumor, so the present case is only the fifth case in the world. Despite. the very poor prognosis of patients with pheochromocytoma and malignant peripheral nerve sheath tumors reported in the literature, the patient remains well without evidence of recurrence or new metastatic lesions at 36 months postoperatively. Copyright (C) 2012, Asian Surgical Association. Published by Elsevier Taiwan LLC.

引用

页码：187 / 190

页数：4

共 9 条

[1] NEUROCRISTOPATHIES - UNIFYING CONCEPT OF DISEASE ARISING IN NEURAL CREST MALDEVELOPMENT [J].