Tricuspid atresia with absent pulmonary valve and intact ventricular septum: successful bidirectional cavopulmonary anastomosis with complete exclusion of the right ventricle

被引：2
作者：
Lee, Cheul [1 ]
Kim, Kyung Min [2 ]
Lee, Jae Young [2 ]
Yoon, Jihong [2 ]
机构：
[1] Catholic Univ Korea, Seoul St Marys Hosp, Dept Thorac & Cardiovasc Surg, Coll Med, 222 Banpo Daero, Seoul 06591, South Korea
[2] Catholic Univ Korea, Seoul St Marys Hosp, Dept Pediat, Coll Med, Seoul, South Korea
来源：
CARDIOLOGY IN THE YOUNG | 2020年 / 30卷 / 01期
关键词：
Tricuspid atresia; absent pulmonary valve; intact ventricular septum; bidirectional cavopulmonary anastomosis; CONGENITAL ABSENCE;
D O I：
10.1017/S1047951119002749
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Tricuspid atresia with absent pulmonary valve and intact ventricular septum is an extremely rare cardiac malformation, historically associated with a poor prognosis. Only a few cases with successful surgical palliation have been reported in the literature. We present the case of an 8-month-old infant with this malformation who underwent successful bidirectional cavopulmonary anastomosis with complete exclusion of the right ventricle.
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收藏
页码：126 / 128
页数：3
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