Cardiac pseudoturnor revealing Behcet's disease

Introduction. - Cardiac thrombosis is a rare complication of Behcet's disease (BD), which may present as a cardiac tumor. Its discovery precedes, in half of the cases, the diagnosis of BD. The high mortality may be associated to postsurgical complications and/or an associated involvement of pulmonary arteries. Case report. - We present the case of a 31 years old Caucasian French woman, with a history of venous thromboembolic disease, who had surgery after the discovery of a right ventricle tumor. That was an organised thrombus with endomyocardial fibrosis and a diagnosis of Behcet's disease was made after the surgery. The outcome was favourable under medical treatment associating corticosteroids, colchicine and antivitamin K (AVK), without relapse four years later. Conclusion. - The discovery of an intracardiac mass in a young patient must evoke the diagnosis of cardiac thrombus and Behcet's disease, even in the absence of predisposing ethnic or geographic factor. (c) 2005 Elsevier SAS. Tous droits reserves.