Transabdominal Intrapericardial Approach in Liver Transplantation for Unresectable Primary Hepatic Functioning Paraganglioma With Invasion Into Hepatic Veins and Suprahepatic Vena Cava: A Surgical and Anesthesia Management Challenge

被引：2

作者：

Kim, J. ^{[1
,2
]}

Fons, R. A. ^{[2
,3
]}

Scott, J. P. ^{[2
,3
]}

Eriksen, C. M. ^{[1
,2
]}

Lerret, S. M. ^{[2
,4
]}

Browning, M. B. ^{[2
,5
]}

Telega, G. W. ^{[2
,4
]}

Vitola, B. E. ^{[2
,4
]}

Hoffman, G. M. ^{[2
,3
]}

North, P. E. ^{[2
,3
]}

Vo, N. N. ^{[2
,6
]}

Zimmerman, M. A. ^{[1
,2
]}

Hong, J. C. ^{[1
,2
]}

机构：

[1] Med Coll Wisconsin, Div Transplant Surg, Milwaukee, WI 53226 USA

[2] Childrens Hosp Wisconsin, Milwaukee, WI 53201 USA

[3] Med Coll Wisconsin, Dept Anesthesiol, Milwaukee, WI 53226 USA

[4] Med Coll Wisconsin, Div Gastroenterol & Hepatol, Milwaukee, WI 53226 USA

[5] Med Coll Wisconsin, Div Hematol Oncol Bone Marrow Transplant, Milwaukee, WI 53226 USA

[6] Med Coll Wisconsin, Div Pediat Radiol, Milwaukee, WI 53226 USA

来源：

TRANSPLANTATION PROCEEDINGS | 2018年 / 50卷 / 09期

关键词：

PHEOCHROMOCYTOMA; DIAGNOSIS;

D O I：

10.1016/j.transproceed.2018.02.189

中图分类号：

R392 [医学免疫学]; Q939.91 [免疫学];

学科分类号：

100102 ;

摘要：

Primary hepatic functional paraganglioma is a rare form of extra-adrenal catecholamine-secreting tumor. Definitive treatment of functioning paraganglioma is challenging because of the critical location of the tumor frequently in close proximity to vital structures and risk of excessive catecholamine release during operative manipulation. We report the multi-disciplinary management approach for a case of unresectable primary hepatic functional paraganglioma with invasion into the hepatic veins and suprahepatic vena cava. To our knowledge, this is the first report showing that orthotopic liver transplantation is curative for patients with unresectable primary hepatic paraganglioma. For locally advanced unresectable hepatic paraganglioma that involves the intrapericardial vena cava, a meticulous pre- and intraoperative medical management and transabdominal intrapericardial vascular control of the suprahepatic vena cava during orthotopic liver transplantation allows for complete extirpation of the tumor and achieves optimal outcome.

引用

页码：2630 / 2635

页数：6