Foramen magnum decompression and expansile duroplasty for acquired Chiari type I malformation in craniometaphyseal dysplasia

被引：10

作者：

Sewell, M. D. ^{[1
,2
]}

Akram, H. ^{[1
,2
]}

Wadley, J. ^{[1
,2
]}

机构：

[1] St Bartholomews Hosp, Dept Neurosurg, London E1 1BB, England

[2] Royal London Hosp, London E1 1BB, England

来源：

BRITISH JOURNAL OF NEUROSURGERY | 2008年 / 22卷 / 01期

关键词：

craniometaphyseal dysplasia; Chiari malformation; foramen magnum decompression;

D O I：

10.1080/02688690701658737

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Craniometaphyseal dysplasia (CMD) is a rare genetic bone remodelling disorder characterized by undertubulation of the long bones and sclerosis and hyperostosis of the skull base with cranial nerve impairment. To our knowledge there are no previous reported cases of autosomal dominant CMD and acquired Chiari type 1 malformation with cervicomedullary compression. We outline the clinical and radiological features of this condition and describe the surgical management.

引用

页码：83 / 85

页数：3