Dentatorubral-pallidoluysian atrophy (DRPLA) presenting with psychosis

被引:14
作者
Adachi, N
Arima, K
Asada, T
Kato, N
Minami, N
Goto, Y
Onuma, T
Ikeuchi, T
Tsuji, S
Hayashi, M
Fukutani, Y
机构
[1] Adachi Mental Clin, Sapporo, Hokkaido 0040867, Japan
[2] Natl Ctr Neurol & Psychiat, Kodaira, Tokyo, Japan
[3] Tokyo Inst Psychiat, Tokyo, Japan
[4] Niigata Univ, Brain Res Inst, Dept Neurol, Niigata 951, Japan
[5] Natl Hokuriku Hosp, Joana, Japan
[6] Fukui Univ, Dept Neuropsychiat, Fukui 910, Japan
关键词
D O I
10.1176/appi.neuropsych.13.2.258
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The authors report an four DRPLA patients who manifested delusions. All patients demonstrated autosomal dominant DRPLA confirmed by standard gene analysis. Patients with DRPLA can exhibit a variety of psychiatric symptoms in addition to extrapyramidal and cerebellar symptoms.
引用
收藏
页码:258 / 260
页数:3
相关论文
共 10 条
  • [1] Adachi N, 1992, SEISHIN IGAKU, V34, P745
  • [2] DENTATORUBRAL-PALLIDOLUYSIAN ATROPHY AND HAW-RIVER-SYNDROME
    BURKE, AR
    IKEUCHI, T
    KOIDE, R
    TSUJI, S
    YAMADA, M
    PERICAKVANCE, MA
    VANCE, JM
    [J]. LANCET, 1994, 344 (8938) : 1711 - 1712
  • [3] DENTATORUBRAL-PALLIDOLUYSIAN ATROPHY - CLINICAL-FEATURES ARE CLOSELY-RELATED TO UNSTABLE EXPANSIONS OF TRINUCLEOTIDE (CAG) REPEAT
    IKEUCHI, T
    KOIDE, R
    TANAKA, H
    ONODERA, O
    IGARASHI, S
    TAKAHASHI, H
    KONDO, R
    ISHIKAWA, A
    TOMODA, A
    MIIKE, T
    SATO, K
    IHARA, Y
    HAYABARA, T
    ISA, F
    TANABE, H
    TOKIGUCHI, S
    HAYASHI, M
    SHIMIZU, N
    IKUTA, F
    NAITO, H
    TSUJI, S
    [J]. ANNALS OF NEUROLOGY, 1995, 37 (06) : 769 - 775
  • [4] Inatsuki G, 1990, SEISHIN IGAKU, V32, P1135
  • [5] UNSTABLE EXPANSION OF CAG REPEAT IN HEREDITARY DENTATORUBRAL-PALLIDOLUYSIAN ATROPHY (DRPLA)
    KOIDE, R
    IKEUCHI, T
    ONODERA, O
    TANAKA, H
    IGARASHI, S
    ENDO, K
    TAKAHASHI, H
    KONDO, R
    ISHIKAWA, A
    HAYASHI, T
    SAITO, M
    TOMODA, A
    MIIKE, T
    NAITO, H
    IKUTA, F
    TSUJI, S
    [J]. NATURE GENETICS, 1994, 6 (01) : 9 - 13
  • [6] MORITA M, 1986, SEISHIN IGAKU, V28, P1027
  • [7] NAITO H, 1982, NEUROLOGY, V32, P789
  • [8] Naito H, 1987, PSYCHIAT NEUROL JPN, V74, P871
  • [9] HEREDITARY DENTATORUBRAL-PALLIDOLUYSIAN ATROPHY - CLINICAL AND PATHOLOGIC VARIANTS IN A FAMILY
    TAKAHASHI, H
    OHAMA, E
    NAITO, H
    TAKEDA, S
    NAKASHIMA, S
    MAKIFUCHI, T
    IKUTA, F
    [J]. NEUROLOGY, 1988, 38 (07) : 1065 - 1070
  • [10] A CLINICAL AND MOLECULAR-GENETIC STUDY OF DENTATORUBROPALLIDOLUYSIAN ATROPHY IN 4 EUROPEAN FAMILIES
    WARNER, TT
    WILLIAMS, LD
    WALKER, RWH
    FLINTER, F
    ROBB, SA
    BUNDEY, SE
    HONAVAR, M
    HARDING, AE
    [J]. ANNALS OF NEUROLOGY, 1995, 37 (04) : 452 - 459