Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum
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作者:
Seguela, Pierre-Emmanuel
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Hop Enfants, F-31059 Toulouse 9, France
Ctr Chirurg Marie Lannelongue, Dept Pediat Cardiol, Le Plessis Robinson, FranceHop Enfants, F-31059 Toulouse 9, France
Seguela, Pierre-Emmanuel
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Houyel, Lucile
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Ctr Chirurg Marie Lannelongue, Dept Pediat Cardiol, Le Plessis Robinson, FranceHop Enfants, F-31059 Toulouse 9, France
We report the case of a newborn with pulmonary atresia with intact ventricular septum and right ventricle-dependent coronary circulation. He died several weeks after a Blalock-Taussig procedure because of a progressive stenosis of the main coronary artery. We present echocardiographic and dual-source CT images of the stenosis, with autopsy correlation. To our knowledge, CT images of this quality have never been reported in a newborn. This case illustrates the extreme difficulty in prognosticating the outcome for these patients and underlines the need for a detailed neonatal coronary mapping to assess right ventricle-dependent coronary circulation.
机构:
St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Peterson, Renuka E.
Freire, Grace
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St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Johns Hopkins All Childrens Hosp, Johns Hopkins All Childrens Heart Inst, Pediat & Fetal Cardiol, 601 5th St South, St Petersburg, FL 33701 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Freire, Grace
Marino, Cynthia J.
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St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Marino, Cynthia J.
Jureidini, Saadeh B.
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机构:
St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Joseph Boon Gregg Missouri Endowed Chair, Kansas City, MO USA
Univ Missouri Kansas City, Sch Med, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Lofland, Gary K.
O'Brien, James E., Jr.
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机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Univ Missouri Kansas City, Sch Med, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
O'Brien, James E., Jr.
Swihart, Jennifer A.
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h-index: 0
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Swihart, Jennifer A.
Stroup, Richard E.
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h-index: 0
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Heart Ctr Informat, Cardiovasc Surg, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Stroup, Richard E.
Kaine, Stephen F.
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机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Univ Missouri Kansas City, Sch Med, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
机构:
St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Peterson, Renuka E.
Freire, Grace
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h-index: 0
机构:
St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Johns Hopkins All Childrens Hosp, Johns Hopkins All Childrens Heart Inst, Pediat & Fetal Cardiol, 601 5th St South, St Petersburg, FL 33701 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Freire, Grace
Marino, Cynthia J.
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h-index: 0
机构:
St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
Marino, Cynthia J.
Jureidini, Saadeh B.
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h-index: 0
机构:
St Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USASt Louis Univ, Sch Med, SSM Hlth Cardinal Glennon Childrens Hosp, Div Pediat Cardiol, 1465 S Grand Blvd, St Louis, MO 63104 USA
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Joseph Boon Gregg Missouri Endowed Chair, Kansas City, MO USA
Univ Missouri Kansas City, Sch Med, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Lofland, Gary K.
O'Brien, James E., Jr.
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Univ Missouri Kansas City, Sch Med, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
O'Brien, James E., Jr.
Swihart, Jennifer A.
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Swihart, Jennifer A.
Stroup, Richard E.
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Heart Ctr Informat, Cardiovasc Surg, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Stroup, Richard E.
Kaine, Stephen F.
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA
Univ Missouri Kansas City, Sch Med, Columbia, MO USAChildrens Mercy Hosp & Clin, 2401 Gillham Rd, Kansas City, MO 64108 USA