Kaposiform hemangioendothelioma of the choledochus

被引:12
|
作者
Terui, Keita [1 ,2 ]
Nakatani, Yukio [2 ]
Kambe, Michiyo [2 ]
Fukunaga, Masaharu [3 ]
Hishiki, Tomoro [1 ,2 ]
Saito, Takeshi [1 ,2 ]
Sato, Yoshiharu [1 ,2 ]
Takenouchi, Ayako [1 ,2 ]
Saito, Eriko [1 ,2 ]
Ono, Sachie [1 ,2 ]
Yoshida, Hideo [1 ,2 ]
机构
[1] Chiba Univ, Dept Pediat Surg, Grad Sch Med, Chiba 2608677, Japan
[2] Chiba Univ, Dept Diagnost Pathol, Grad Sch Med, Chiba 2608677, Japan
[3] Jikei Univ, Dept Pathol, Jikei Daisan Hosp, Sch Med, Tokyo 105, Japan
关键词
Jaundice; Hemangioendothelioma; Vascular tumor; Kaposiform hemangioendothelioma; Choledochus; Infant; OBSTRUCTIVE-JAUNDICE; VASCULAR TUMORS; CHILDHOOD; HEMANGIOMA; INFANCY;
D O I
10.1016/j.jpedsurg.2010.05.031
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Kaposiform hemangioendothelioma (KHE) is a rare, locally aggressive vascular neoplasm that mainly occurs during childhood. Although KHE may involve various organs, involvement of the choledochus has not been reported. We report a case of KHE in a 5-month-old male infant. The patient was admitted with icterus and acholic stool. Contrast computed tomography revealed a vascular tumor in the hepatic portal region causing biliary obstruction. Excision of the extrahepatic duct and hepatoportoenterostomy were performed successfully, and he has been well during 3 years of postoperative follow-up. (C) 2010 Elsevier Inc. All rights reserved.
引用
收藏
页码:1887 / 1889
页数:3
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