Mouse models of neurofibromatosis

被引:15
作者
McClatchey, AI [1 ]
Cichowski, K
机构
[1] MGH Canc Ctr, Charlestown, MA 02129 USA
[2] Harvard Univ, Sch Med, Dept Pathol, Charlestown, MA 02129 USA
[3] Brigham & Womens Hosp, Dept Med, Div Genet, Boston, MA 02115 USA
[4] Harvard Univ, Sch Med, Boston, MA 02115 USA
来源
BIOCHIMICA ET BIOPHYSICA ACTA-REVIEWS ON CANCER | 2001年 / 1471卷 / 02期
关键词
neurofibromatosis; mouse; malignant peripheral; nerve sheath tumor;
D O I
10.1016/S0304-419X(00)00026-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
[No abstract available]
引用
收藏
页码:M73 / M80
页数:8
相关论文
共 31 条
[1]   TARGETED DISRUPTION OF THE NEUROFIBROMATOSIS TYPE-1 GENE LEADS TO DEVELOPMENTAL ABNORMALITIES IN HEART AND VARIOUS NEURAL CREST-DERIVED TISSUES [J].
BRANNAN, CI ;
PERKINS, AS ;
VOGEL, KS ;
RATNER, N ;
NORDLUND, ML ;
REID, SW ;
BUCHBERG, AM ;
JENKINS, NA ;
PARADA, LF ;
COPELAND, NG .
GENES & DEVELOPMENT, 1994, 8 (09) :1019-1029
[2]   A MAJOR SEGMENT OF THE NEUROFIBROMATOSIS TYPE-1 GENE - CDNA SEQUENCE, GENOMIC STRUCTURE, AND POINT MUTATIONS [J].
CAWTHON, RM ;
WEISS, R ;
XU, GF ;
VISKOCHIL, D ;
CULVER, M ;
STEVENS, J ;
ROBERTSON, M ;
DUNN, D ;
GESTELAND, R ;
OCONNELL, P ;
WHITE, R .
CELL, 1990, 62 (01) :193-201
[3]   Mouse models of tumor development in neurofibromatosis type 1 [J].
Cichowski, K ;
Shih, TS ;
Schmitt, E ;
Santiago, S ;
Reilly, K ;
McLaughlin, ME ;
Bronson, RT ;
Jacks, T .
SCIENCE, 1999, 286 (5447) :2172-2176
[4]  
ERNARDS A, 2000, TUMOR SUPPRESSOR GEN
[5]   MULTIPLE CELL ORIGIN OF HEREDITARY NEUROFIBROMAS [J].
FIALKOW, PJ ;
SAGEBIEL, RW ;
GARTLER, SM ;
RIMOIN, DL .
NEW ENGLAND JOURNAL OF MEDICINE, 1971, 284 (06) :298-&
[6]  
Giovannini M, 2000, GENE DEV, V14, P1617
[7]   Schwann cell hyperplasia and tumors in transgenic mice expressing a naturally occurring mutant NF2 protein [J].
Giovannini, M ;
Robanus-Maandag, E ;
Niwa-Kawakita, M ;
van der Valk, M ;
Woodruff, JM ;
Goutebroze, L ;
Mérel, P ;
Berns, A ;
Thomas, G .
GENES & DEVELOPMENT, 1999, 13 (08) :978-986
[8]   Requirement of Drosophila NF1 for activation of adenylyl cyclase by PACAP38-like neuropeptides [J].
Guo, HF ;
The, I ;
Hannan, F ;
Bernards, A ;
Zhong, Y .
SCIENCE, 1997, 276 (5313) :795-798
[9]  
Huynh DP, 1996, ONCOGENE, V13, P73
[10]   TUMOR PREDISPOSITION IN MICE HETEROZYGOUS FOR A TARGETED MUTATION IN NF1 [J].
JACKS, T ;
SHIH, TS ;
SCHMITT, EM ;
BRONSON, RT ;
BERNARDS, A ;
WEINBERG, RA .
NATURE GENETICS, 1994, 7 (03) :353-361