Cutaneous mastocytosis in the adult: what lies beneath

被引：0
作者：
Torres, Liliana [1 ]
Soares, Francisco Bento [1 ]
Anjos, Diana Pereira [1 ]
Mesquita, Mari [1 ]
机构：
[1] Ctr Hosp Tamega & Sousa, Guilhufe Penafiel, Portugal
来源：
GALICIA CLINICA | 2020年 / 81卷 / 01期
关键词：
Mastocytosis; Mast cells; Darier's sign; MAST-CELL;
D O I：
10.22546/55/1820
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Mastocytosis is a disorder characterized by clonal mast cell proliferation and accumulation within various organs, most commonly, the skin. Adult-onset mastocytosis is highly suggestive of a systemic involvement and the cases limited to the skin are uncommon. The authors report a 61-year-old male with pruritus associated with hyperpigmented maculopapular skin lesions and a positive Darier's sign. The skin biopsy revealed spindle mast cells infiltrations. The bone marrow study was normal. He started on H1 antihistamines with significant clinical improvement.
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收藏
页码：19 / 20
页数：2
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