Malignant occipital astrocytoma in a patient with Lhermitte-Duclos disease (cerebellar dysplastic gangliocytoma)

被引:6
作者
Domingo, Z [1 ]
FisherJeffes, ND [1 ]
DeVilliers, JC [1 ]
机构
[1] UNIV CAPE TOWN,GROOTE SCHUUR HOSP,DEPT NEUROSURG,CAPE TOWN 7925,SOUTH AFRICA
关键词
cerebellum; dysplastic gangliocytoma; Lhermitte-Duclos disease; malignant cerebral astrocytoma;
D O I
10.1080/02688699650040610
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A case of Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum) is described. Seventeen years after the diagnosis was made, the patient developed a malignant astrocytoma of the cerebrum, an association only once previously reported. The clinical presentation and radiological features are presented.
引用
收藏
页码:99 / 102
页数:4
相关论文
共 17 条
[1]   LHERMITTE-DUCLOS DISEASE (GRANULE CELL HYPERTROPHY OF CEREBELLUM) PATHOLOGICAL ANALYSIS OF FIRST FAMILIAL CASES [J].
AMBLER, M ;
POGACAR, S ;
SIDMAN, R .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1969, 28 (04) :622-&
[2]   LHERMITTE-DUCLOS DISEASE - CT AND MR FINDINGS [J].
ASHLEY, DG ;
ZEE, CS ;
CHANDRASOMA, PT ;
SEGALL, HD .
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1990, 14 (06) :984-987
[3]  
CARBONE F, 1955, Acta Neurol Psychiatr Belg, V55, P568
[4]   PREOPERATIVE DIAGNOSIS OF LHERMITTE-DUCLOS DISEASE BY MAGNETIC-RESONANCE IMAGING - CASE-REPORT [J].
CARTER, JE ;
MERREN, MD ;
SWANN, KW .
JOURNAL OF NEUROSURGERY, 1989, 70 (01) :135-137
[5]   SO-CALLED GANGLIOCYTOMA OF CEREBELLUM - REPORT OF A CASE [J].
CHRISTIAN, H .
JOURNAL OF NEUROSURGERY, 1961, 18 (01) :125-&
[6]   DYSPLASTIC GANGLIOCYTOMA AND INTRACTABLE PARTIAL SEIZURES IN CHILDHOOD [J].
DUCHOWNY, MS ;
RESNICK, TJ ;
ALVAREZ, L .
NEUROLOGY, 1989, 39 (04) :602-604
[7]  
GESAGGA EC, 1980, NEUROSURG REV, V3, P151
[8]  
HABERLAND C, 1977, HDB CLIN NEUROLOGY C, V33, P1
[9]   MAGNETIC-RESONANCE-IMAGING OF GANGLION-CELL TUMORS [J].
HASHIMOTO, M ;
FUJIMOTO, K ;
SHINODA, S ;
MASUZAWA, T .
NEURORADIOLOGY, 1993, 35 (03) :181-184
[10]   COWDENS DISEASE - A POSSIBLE NEW SYMPTOM COMPLEX WITH MULTIPLE SYSTEM INVOLVEMENT [J].
LLOYD, KM ;
DENNIS, M .
ANNALS OF INTERNAL MEDICINE, 1963, 58 (01) :136-+