Scleromyxedema is an uncommon disease, affecting the skin mainly and other internal organs sometimes, characterized by fibroblasts proliferation, fibrosis, and mucous deposition in the absence of thyroid disorder. It is associated with monoclonal gammopathy in most cases. We are reporting a case with a rare presentation of tumoral scleromyxedema in the neck, with a mass mimicking other tumoral lesions, highlighting the importance of diagnosis and histopathologic correlation.
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Bichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Brunet-Possenti, Florence
Hermine, Olivier
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Univ Paris 05, Necker Hosp, AP HP, Dept Hematol, F-75270 Paris 06, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Hermine, Olivier
Marinho, Eduardo
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Bichat Claude Bernard Hosp, AP HP, Dept Anatomopathol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Marinho, Eduardo
Crickx, Beatrice
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Bichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Crickx, Beatrice
Descamps, Vincent
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机构:
Bichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
机构:
Bichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Brunet-Possenti, Florence
Hermine, Olivier
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, Necker Hosp, AP HP, Dept Hematol, F-75270 Paris 06, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Hermine, Olivier
Marinho, Eduardo
论文数: 0引用数: 0
h-index: 0
机构:
Bichat Claude Bernard Hosp, AP HP, Dept Anatomopathol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Marinho, Eduardo
Crickx, Beatrice
论文数: 0引用数: 0
h-index: 0
机构:
Bichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France
Crickx, Beatrice
Descamps, Vincent
论文数: 0引用数: 0
h-index: 0
机构:
Bichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, FranceBichat Claude Bernard Hosp, AP HP, Dept Dermatol, F-75877 Paris 18, France