Congenitally Corrected Transposition of Great Arteries with Dextrocardia, Patent Ductus Arteriosus, Atrial Septal Defects and Ventricular Septal Defects in a 15-Year-Old Marfanoid Habitus Patient: A Case Study

被引:3
作者
Munaf, Misbah [1 ]
Farooqui, Sofia [1 ]
Kazmi, Syeda K. [1 ]
Ul-Haque, Ibtehaj [1 ]
机构
[1] Dow Univ Hlth Sci, Internal Med, Karachi, Pakistan
关键词
dextrocardia; patent ductus arteriosus; atrial septal defect; marfanoid habitus; pulmonary atresia; ventricular septal defect; congenitally corrected transposition of the great arteries; DISEASE; ADULTS;
D O I
10.7759/cureus.8937
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital cardiac anomaly defined by atrio-ventricular and ventriculo-arterial discordance. This malformation makes up less than 1% of congenital heart defects. We report here a case of a 15-year-old female who presented to our hospital with dyspnea as seen in the New York Heart Association (NYHA) Functional Classification class III and hemoptysis. She was clinically found to have marfanoid habitus, and subsequent echocardiographic study disclosed CCTGA-associated with Ebstein's anomaly, ventricular septal defect, left ventricular outflow obstruction, right ventricular outflow obstruction, co-existing dextrocardia, atrial septal defect, patent ductus arteriosus, non-confluent pulmonary arteries, and pulmonary atresia. This case highlights the association between such rare cardiac conditions. To the best of our knowledge, this is the first case of CCTGA at a young age, with the aforementioned abnormalities documented in the literature reported from Pakistan.
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页数:8
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