Treatment of thrombotic thrombocytopenic purpura

被引：1

作者：

Galstyan, Gennadii M. ^{[1
]}

Maschan, Alexei A. ^{[2
]}

Klebanova, Elizaveta E. ^{[1
]}

Kalinina, Irina I. ^{[2
]}

机构：

[1] Natl Res Ctr Hematol, Moscow, Russia

[2] Rogachev Natl Med Res Ctr Pediat Hematol Oncol &, Moscow, Russia

来源：

TERAPEVTICHESKII ARKHIV | 2021年 / 93卷 / 07期

关键词：

ADAMTS13; thrombotic thrombocytopenic purpura; Upshaw-Schulman syndrome; pregnancy; therapeutic plasma exchange; recombinant ADAMTS13; UPSHAW-SCHULMAN SYNDROME; VON-WILLEBRAND-FACTOR; PLASMA-EXCHANGE; ADAMTS13; MANAGEMENT; THERAPY; ONSET;

D O I：

10.26442/00403660.2021.07.200914

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The review discusses approaches to treatment of congenital thrombotic thrombocytopenic purpura (TTP) or Upshaw-Schulman syndrome. In congenital TTP, plasma transfusions are sufficient. Such treatment options as plasma exchange, administration of clotting factor VIII concentrate, recombinant ADAMTS13, are also used. Separately discussed issues of management of patients with TTP during pregnancy, and pediatric patients with TTP.

引用

页码：826 / 829

页数：4

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