X-linked protoporphyria: Iron supplementation improves protoporphyrin overload, liver damage and anaemia

被引：28
作者：
Landefeld, Christoph [1 ]
Kentouche, Karim [1 ]
Gruhn, Bernd [1 ]
Stauch, Thomas [2 ]
Roessler, Steve [3 ]
Schuppan, Detlef [4 ]
Whatley, Sharon D. [5 ]
Beck, James F. [1 ]
Stoelzel, Ulrich [3 ]
机构：
[1] Univ Jena, Sch Med, Dept Paediat, Jena, Germany
[2] MVZ Labor PD Dr Volkmann & Kollegen, Karlsruhe, Germany
[3] Klinikum Chemnitz, Dept Internal Med 2, Chemnitz, Germany
[4] Johannes Gutenberg Univ Mainz, Dept Med 1, Sch Med, Mainz, Germany
[5] Univ Wales Hosp, Dept Med Biochem & Immunol, Cardiff CF4 4XW, S Glam, Wales
来源：
BRITISH JOURNAL OF HAEMATOLOGY | 2016年 / 173卷 / 03期
关键词：
porphyria; iron; liver disease; erythropoiesis; haem biosynthesis; ERYTHROPOIETIC PROTOPORPHYRIA; THERAPY;
D O I：
10.1111/bjh.13612
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
引用
收藏
页码：482 / 484
页数：3
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