Behcet's syndrome: providing integrated care

被引:33
作者
Esatoglu, Sinem Nihal [1 ]
Kutlubay, Zekayi [2 ]
Ucar, Didar [3 ]
Hatemi, Ibrahim [4 ]
Uygunoglu, Ugur [5 ]
Siva, Aksel [5 ]
Hatemi, Gulen [1 ]
机构
[1] Istanbul Univ, Dept Internal Med, Div Rheumatol, Istanbul, Turkey
[2] Istanbul Univ, Dept Dermatol, Istanbul, Turkey
[3] Istanbul Univ, Dept Ophthalmol, Istanbul, Turkey
[4] Istanbul Univ, Dept Internal Med, Div Gastroenterol, Istanbul, Turkey
[5] Istanbul Univ, Cerrahpasa Med Fac, Dept Neurol, Istanbul, Turkey
关键词
Behcet disease; multidisciplinary care; diagnosis; treatment; vasculitis; epidemiology; management; GENOME-WIDE ASSOCIATION; CLINICAL CHARACTERISTICS; PAPULOPUSTULAR LESIONS; INTRACARDIAC THROMBUS; PATHERGY REACTION; OUTCOME SURVEY; DISEASE; INVOLVEMENT; MANIFESTATIONS; SACROILIITIS;
D O I
10.2147/JMDH.S93681
中图分类号
R19 [保健组织与事业(卫生事业管理)];
学科分类号
摘要
Behcet's syndrome (BS) is a multisystem vasculitis that presents with a variety of mucocutaneous manifestations such as oral and genital ulcers, papulopustular lesions and erythema nodosum as well as ocular, vascular, gastrointestinal and nervous system involvement. Although it occurs worldwide, it is especially prevalent in the Far East and around the Mediterranean Sea. Male gender and younger age at disease onset are associated with a more severe disease course. The management of BS depends on the severity of symptoms. If untreated, morbidity and mortality are considerably high in patients with major organ involvement. Multidisciplinary patient care is essential for the management of BS, as it is for other multisystem diseases. Rheumatologists, dermatologists, ophthalmologists, neurologists, cardiovascular surgeons and gastroenterologists are members of the multidisciplinary team. In this study, we reviewed the epidemiology, etiology, diagnostic criteria sets, clinical findings and treatment of BS and highlighted the importance of the multidisciplinary team in the management of BS.
引用
收藏
页码:309 / 319
页数:11
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