Unmasking dermatofibrosarcoma protuberans: Case report of an atypical presentation complicated by post-surgical excision
被引:3
作者:
Zhou , YaQun
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机构:
Touro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
St Clares Denville Hosp, Dept Surg, Denville, NJ USATouro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
Zhou , YaQun
[1
,2
]
Chin, Justin
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机构:
Touro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
Lifelong Med Care, Dept Family Med, Richmond, CA USATouro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
Chin, Justin
[1
,3
]
Strutin, Millard D.
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机构:
St Clares Denville Hosp, Dept Surg, Denville, NJ USATouro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
Strutin, Millard D.
[2
]
Lomiguen, Christine M.
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机构:
Lake Erie Coll Osteopath Med, Dept Pathol, Erie, PA USATouro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
Lomiguen, Christine M.
[4
]
机构:
[1] Touro Coll Osteopath Med, Dept Primary Care, New York, NY 10027 USA
[2] St Clares Denville Hosp, Dept Surg, Denville, NJ USA
[3] Lifelong Med Care, Dept Family Med, Richmond, CA USA
[4] Lake Erie Coll Osteopath Med, Dept Pathol, Erie, PA USA
来源:
INTERNATIONAL JOURNAL OF SURGERY CASE REPORTS
|
2020年
/
69卷
关键词:
Dermatofibrosarcoma protuberans;
DFSP;
Soft tissue tumor;
Lipoma;
CD34;
Case report;
WIDE LOCAL EXCISION;
COL1A1-PDGFB;
DIAGNOSIS;
FUSION;
D O I:
10.1016/j.ijscr.2020.03.020
中图分类号:
R61 [外科手术学];
学科分类号:
摘要:
INTRODUCTION: Dermatofibrosarcoma Protuberans (DFSP) is a rare type of malignant tumor of the cutaneous soft tissue that typically involves the dermis and surrounding structures. The typical clinical presentation involves an asymptomatic, slowly enlarging, indurated plaque, usually found on the trunk. PRESENTATION OF CASE: Here we present an atypical presentation of DFSP in a patient with a recurrent mass that was initially diagnosed as a lipoma, with supporting literature and clinical considerations for post-surgical management DISCUSSION: In its earlier stages, DFSP can mimic other benign or malignant dermatological pathologies, which can complicate diagnosis purely via history and physical exam. Atypical features such as prior surgical management, morphology, and location can complicate the clinical diagnosis of DFSP. Immunohistochemistry is often required for definitive diagnosis as DFSP is CD34+ and is histologically described as spindle-cells in whorled or storiform pattern, with uniform, small elongated cells. CONCLUSION: DFSP is a rare tumor of the skin and subcutaneous tissue. Though it commonly presents with induration, skin discoloration, and telangiectasias, it is important to keep DFSP as a differential in new masses found on previous surgical sites, especially if the previous mass had a possibility of recurrence. (C) 2020 The Author( s). Published by Elsevier Ltd on behalf of BS Publishing Group Ltd.
机构:
Newcastle Tyne Hosp NHS Fdn Trust, Dept Plast Surg, Royal Victoria Infirm, Newcastle Upon Tyne, Tyne & Wear, EnglandChelsea & Westminster Hosp NHS Fdn Trust, London, England
Koshy, Kiron
Fowler, Alexander J.
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机构:
Royal London Hosp, Crit Care & Perioperat Med Res Grp, London, EnglandChelsea & Westminster Hosp NHS Fdn Trust, London, England
Fowler, Alexander J.
Orgill, Dennis P.
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机构:
Brigham & Womens Hosp, Div Plast Surg, Boston, MA 02115 USA
Harvard Med Sch, Boston, MA 02115 USAChelsea & Westminster Hosp NHS Fdn Trust, London, England
Orgill, Dennis P.
Zhu, Hongyi
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机构:
Univ Arizona, Tucson, AZ 85721 USAChelsea & Westminster Hosp NHS Fdn Trust, London, England
机构:
Newcastle Tyne Hosp NHS Fdn Trust, Dept Plast Surg, Royal Victoria Infirm, Newcastle Upon Tyne, Tyne & Wear, EnglandChelsea & Westminster Hosp NHS Fdn Trust, London, England
Koshy, Kiron
Fowler, Alexander J.
论文数: 0引用数: 0
h-index: 0
机构:
Royal London Hosp, Crit Care & Perioperat Med Res Grp, London, EnglandChelsea & Westminster Hosp NHS Fdn Trust, London, England
Fowler, Alexander J.
Orgill, Dennis P.
论文数: 0引用数: 0
h-index: 0
机构:
Brigham & Womens Hosp, Div Plast Surg, Boston, MA 02115 USA
Harvard Med Sch, Boston, MA 02115 USAChelsea & Westminster Hosp NHS Fdn Trust, London, England
Orgill, Dennis P.
Zhu, Hongyi
论文数: 0引用数: 0
h-index: 0
机构:
Univ Arizona, Tucson, AZ 85721 USAChelsea & Westminster Hosp NHS Fdn Trust, London, England