Surgery for Hypertrophic Obstructive Cardiomyopathy: Comprehensive LVOT Management beyond Septal Myectomy

被引:13
作者
Affronti, Alessandro [1 ]
Pruna-Guillen, Robert [1 ]
Sandoval, Elena [1 ]
Pereda, Daniel [1 ]
Alcocer, Jorge [1 ]
Castella, Manuel [1 ]
Quintana, Eduard [1 ]
机构
[1] Univ Barcelona, Sch Med, Hosp Clin Barcelona, Inst Clin Cardiovasc,Cardiovasc Surg, C Villarroel 170 Esc 1 5th Floor, Barcelona 08036, Spain
关键词
hypertrophic obstructive cardiomyopathy; systolic anterior motion; septal myectomy; mitral valve; ANTERIOR MITRAL LEAFLET; OUTFLOW TRACT OBSTRUCTION; PAPILLARY-MUSCLE MORPHOLOGY; SUBAORTIC STENOSIS; SURGICAL-MANAGEMENT; ANOMALOUS INSERTION; VALVE ABNORMALITIES; OPERATIVE TREATMENT; ALCOHOL ABLATION; MOTION;
D O I
10.3390/jcm10194397
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Hypertrophic cardiomyopathy (HCM) is a complex, underestimated, multifaceted disease frequently associated with left ventricular outflow tract (LVOT) obstruction. It is clearly demonstrated that this is due not only to septal hypertrophy but also to systolic anterior motion (SAM) of mitral valve leaflets secondary to mitral valve/subvalvular apparatus abnormalities. Surgical treatment involves performing an extended septal myectomy, eventually followed by ancillary procedures to those structures responsible for maintaining LVOT obstruction, if necessary. In this review, we describe the spectrum of possible surgical techniques beyond septal myectomy and their pathophysiologic rationale.
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页数:13
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