Solitary fibrous tumour/haemangiopericytoma of the spinal cord

被引:3
作者
Flores-Justa, Ana [1 ]
Lopez-Garcia, Elena [1 ]
Garcia-Allut, Alfredo [1 ]
Maria Reyes-Santias, Rosa [2 ]
机构
[1] Univ Santiago de Compostela, Hosp Clin, Serv Neurocirugia, Santiago De Compostela, A Coruna, Spain
[2] Univ Santiago de Compostela, Hosp Clin, Serv Anat Patol, Santiago De Compostela, A Coruna, Spain
来源
NEUROCIRUGIA | 2018年 / 29卷 / 06期
关键词
Thoracic; Solitary fibrous tumour; Haemangiopericytoma; Spinal tumour; MRI; CENTRAL-NERVOUS-SYSTEM; TUMOR;
D O I
10.1016/j.neucir.2018.01.005
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
Solitary fibrous tumours/haemangiopericytomas (SFT/HPC) are fibroblastic mesenchymal neoplasms that harbour a genetic fusion of NAB2/STAT6. There are few reported cases in the central nervous system (CNS), of which spinal tumours are minority. We present a case of a 63-year-old woman with progressive paraparesis and a sensory level of T6. On the MRI we detected an intradural extramedullary lesion on T9-T10. We performed a laminectomy with an intraoperative ultrasound study in which we observed a heterogeneous lesion with an infiltrating pattern affecting the medulla at several points, and resection of the lesion. Immunohistological findings revealed positivity for vimentin, CD34 and STAT6; Ki-67 was 2%. A final diagnosis of SFT/HPC with SFT phenotype was made. SFT/HPC of the CNS is a rare neoplasm that should be taken into account in the differential diagnosis of these kinds of lesions, as clinical and MRI findings often lead to errors in diagnostic approach. The support of intraoperative ultrasound can assist in surgical decision-making. (C) 2018 Sociedad Espanola de Neurocirugia. Published by Elsevier Espana, S.L.U. All rights reserved.
引用
收藏
页码:309 / 313
页数:5
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