Hepatosplenic T cell lymphoma responsive to 2′-deoxycoformycin therapy

被引：15

作者：

Bennett, Michael ^{[1
]}

Matutes, Estella ^{[2
]}

Gaulard, Philippe ^{[3
]}

机构：

[1] HaEmek Med Ctr, Dept Haematol, IL-18101 Afula, Israel

[2] Royal Marsden Hosp, Dept Haematol, London SW3 6JJ, England

[3] Henri Mondor Hosp, Dept Pathol, Paris, France

来源：

AMERICAN JOURNAL OF HEMATOLOGY | 2010年 / 85卷 / 09期

关键词：

GAMMA-DELTA; CLINICOPATHOLOGICAL ENTITY; HEMOPHAGOCYTIC SYNDROME; ISOCHROMOSOME; 7Q; NK-CELL; FEATURES; ABNORMALITY; EXPRESSION; ORIGIN;

D O I：

10.1002/ajh.21774

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Hepatosplenic T cell lymphoma (HSTL) is a rare condition usually with an aggresssive course and a poor prognosis even after extensive treatment. We describe here a patient who presented with hemophagocytosis. The lymphoma had unusual phenotypic features, an indolent course and responded to 2'-deoxycoformycin therapy as a single agent. We suggest that this therapy be used in further cases as part of the treatment strategy.

引用

页码：727 / 729

页数：3

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