Klippel-Trenaunay Syndrome with Congenital Heart Disease and Bony Abnormalities: A Rare Case Report

被引：0

作者：

Agarwal, Shail ^{[1
]}

Saini, Shivani ^{[2
]}

Jain, Akshay Kumar ^{[3
]}

机构：

[1] Jhalawar Med Coll, Dept Skin & VD, Jhalawar, India

[2] Dr SN Med Coll, Dept Skin & VD, Jodhpur, India

[3] Govt Med Coll, Dept Skin & VD, Kota, Rajasthan, India

来源：

INDIAN JOURNAL OF PAEDIATRIC DERMATOLOGY | 2022年 / 23卷 / 01期

关键词：

Bony abnormality; congenital heart diseases; Klippel-Trenaunay syndrome; limb hypertrophy; portwine stains; IDENTIFICATION;

D O I：

10.4103/ijpd.ijpd_169_20

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Although Klippel-Trenaunay syndrome (KTS) is an infrequently seen dermatological disorder with plethora of associations. It is largely a clinical diagnosis made by the presence of at least two of the three classic findings. We are reporting a 16-year-old male child who presented to us with the limb hypertrophy, portwine stains, congenital heart disease, and bony abnormality. Multiple associations of KTS make it an interesting case.

引用

页码：58 / 60

页数：3

共 8 条

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