Brugada syndrome (BrS) is an autosomal-dominant condition mainly caused by defects in sodium channels causing ST-segment elevation in electrocardiograms (ECGs) in the V1 and V2 precordial leads, with ventricular tachyarrhythmias due to premature ventricular contractions, which increases the risk of sudden cardiac death. BrS usually presents in adulthood, with an average age of presentation of 41 years. In this article, we describe a case of BrS diagnosed in a 36-year-old male having sudden cardiac arrest with no comorbidities such as hypertension, diabetes mellitus, smoking, or any valvular disease history. We then explain the ECG-based diagnosis, signs and symptoms, presentation at the emergency department, and treatment options.
机构:Univ Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Postema, Pieter G.
Wolpert, Christian
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Univ Hosp Mannheim, Dept Med Cardiol 1, Mannheim, GermanyUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Wolpert, Christian
Amin, Ahmad S.
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Univ Amsterdam, Acad Med Ctr, Heart Failure Res Ctr, NL-1105 AZ Amsterdam, NetherlandsUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Amin, Ahmad S.
Probst, Vincent
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Univ Nantes, CHU Nantes, Serv Cardiol, LInst Thorax, Nantes, France
Univ Nantes, INSERM, UMR 915, Nantes, FranceUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Probst, Vincent
Borggrefe, Martin
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Univ Hosp Mannheim, Dept Med Cardiol 1, Mannheim, GermanyUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Borggrefe, Martin
Roden, Dan M.
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Vanderbilt Univ, Sch Med, Dept Med & Pharmacol, Nashville, TN 37212 USAUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
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Univ Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Univ Amsterdam, Acad Med Ctr, Heart Failure Res Ctr, NL-1105 AZ Amsterdam, NetherlandsUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Tan, Hanno L.
Hiraoka, Masayasu
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Tokyo Med & Dent Univ, Med Res Inst, Dept Cardiovasc Dis, Tokyo, JapanUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
机构:
Univ Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Univ Amsterdam, Acad Med Ctr, Heart Failure Res Ctr, NL-1105 AZ Amsterdam, NetherlandsUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
机构:Univ Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Postema, Pieter G.
Wolpert, Christian
论文数: 0引用数: 0
h-index: 0
机构:
Univ Hosp Mannheim, Dept Med Cardiol 1, Mannheim, GermanyUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Wolpert, Christian
Amin, Ahmad S.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Amsterdam, Acad Med Ctr, Heart Failure Res Ctr, NL-1105 AZ Amsterdam, NetherlandsUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Amin, Ahmad S.
Probst, Vincent
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nantes, CHU Nantes, Serv Cardiol, LInst Thorax, Nantes, France
Univ Nantes, INSERM, UMR 915, Nantes, FranceUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Probst, Vincent
Borggrefe, Martin
论文数: 0引用数: 0
h-index: 0
机构:
Univ Hosp Mannheim, Dept Med Cardiol 1, Mannheim, GermanyUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Borggrefe, Martin
Roden, Dan M.
论文数: 0引用数: 0
h-index: 0
机构:
Vanderbilt Univ, Sch Med, Dept Med & Pharmacol, Nashville, TN 37212 USAUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
机构:
Univ Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Univ Amsterdam, Acad Med Ctr, Heart Failure Res Ctr, NL-1105 AZ Amsterdam, NetherlandsUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Tan, Hanno L.
Hiraoka, Masayasu
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Med & Dent Univ, Med Res Inst, Dept Cardiovasc Dis, Tokyo, JapanUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
机构:
Univ Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands
Univ Amsterdam, Acad Med Ctr, Heart Failure Res Ctr, NL-1105 AZ Amsterdam, NetherlandsUniv Amsterdam, Acad Med Ctr, Dept Cardiol, NL-1105 AZ Amsterdam, Netherlands