Heart transplantation in patients with Emery-Dreifuss muscular dystrophy: Case reports

被引：14

作者：

Dell'Amore, A. ^{[1
]}

Botta, L. ^{[1
]}

Suarez, S. Martin ^{[1
]}

Lo Forte, A. ^{[1
]}

Mikus, E. ^{[1
]}

Camurri, N. ^{[1
]}

Ortelli, L. ^{[1
]}

Arpesella, G. ^{[1
]}

机构：

[1] S Orsola Malpigi Univ Bologna, Heart & Lung Transplantat Program, Bologna, Italy

来源：

TRANSPLANTATION PROCEEDINGS | 2007年 / 39卷 / 10期

关键词：

D O I：

10.1016/j.transproceed.2007.06.076

中图分类号：

R392 [医学免疫学]; Q939.91 [免疫学];

学科分类号：

100102 ;

摘要：

Emery-Dreifuss muscular dystrophy (EDMD) is an hereditary syndrome characterized by slow but progressive locomotor involvement and cardiomyopathy. Cardiac impairment is often the life-limiting feature of the illness. Only a few cases of cardiac transplantation have been reported previously in muscular dystrophy, and only 4 cases of end-stage disease due to EDMD have been treated previously with heart transplantation. Herein we have reported our experince with 2 consecutive patients who underwent heart transplantation for EDMD cardiomyopathy.

引用

页码：3538 / 3540

页数：3

共 12 条

[1]

BAUR X, 1990, KLIN WOCHENSCHR, V237, P316

[2] PROGRESSION OF CARDIAC DISEASE IN EMERY-DREIFUSS MUSCULAR-DYSTROPHY [J].