Angiosarcoma arising from congenital primary lymphedema

被引:7
作者
Janssens, Pauline [1 ]
Dekeuleneer, Valerie [1 ]
Van Damme, An [2 ]
Brouillard, Pascal [3 ]
Revencu, Nicole [4 ]
Clapuyt, Philippe [5 ]
Ferreira, Ingrid [6 ]
Ballieux, Fanny [7 ]
Vikkula, Miikka [3 ,8 ]
Marot, Liliane [6 ]
Baeck, Marie [1 ]
Boon, Laurence M. [3 ,7 ]
机构
[1] Clin Univ St Luc, Dept Dermatol, Brussels, Belgium
[2] Clin Univ St Luc, Dept Pediat Hematooncol, Ctr Vasc Anomalies, Brussels, Belgium
[3] Univ Louvain, de Duve Inst, Human Mol Genet, Brussels, Belgium
[4] Clin Univ St Luc, Dept Clin Genet, Ctr Vasc Anomalies, Brussels, Belgium
[5] Clin Univ St Luc, Dept Pediat Radiol, Ctr Vasc Anomalies, Brussels, Belgium
[6] Clin Univ St Luc, Dept Anatomopathol, Brussels, Belgium
[7] Clin Univ St Luc, Div Plast Surg, Ctr Vasc Anomalies, Brussels, Belgium
[8] Univ Louvain, Walloon Excellence Lifesci & Biotechnol WELBIO, Brussels, Belgium
关键词
angiosarcoma; congenital; lymphangiosarcoma; lymphedema; sirolimus; Stewart-Treves syndrome; STEWART-TREVES-SYNDROME; ANOMALIES; PATIENT; LIMB;
D O I
10.1111/pde.13664
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
We herein report the case of a 3-year-old girl with atypical congenital right upper limb lymphedema who developed an angiosarcoma. Only a few cases have been reported following congenital form of lymphedema and only 4 in such a young child. We also summarize all cases of angiosarcoma associated with congenital lymphedema reported in the literature.
引用
收藏
页码:E382 / E388
页数:7
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