A 63-Year-Old Woman With Neurofibromatosis Type 1 and Pulmonary Hypertension With Worsening Hypoxemia

被引：7

作者：

Chaddha, Udit ^{[1
]}

Puscas, Ioan ^{[1
]}

Prosper, Ashley ^{[2
]}

Ganesh, Sivagini ^{[1
]}

Yaghmour, Bassam ^{[1
]}

机构：

[1] Univ Southern Calif, Keck Sch Med, Div Pulm Crit Care & Sleep Med, 2020 Zonal Ave, Los Angeles, CA 90033 USA

[2] Univ Southern Calif, Keck Sch Med, Dept Radiol, Los Angeles, CA 90033 USA

来源：

CHEST | 2017年 / 152卷 / 04期

关键词：

CAPILLARY HEMANGIOMATOSIS; VENOOCCLUSIVE DISEASE;

D O I：

10.1016/j.chest.2017.05.014

中图分类号：

R4 [临床医学];

学科分类号：

1002 ; 100602 ;

摘要：

A 63-year-old woman with a history of neurofibromatosis type-1 (NF-1) and pulmonary arterial hypertension (PAH) thought to be secondary to the NF-1 presented with a few weeks of worsening dyspnea on exertion. She took no medications other than sildenafil for her pulmonary hypertension (PH). She denied tobacco, alcohol, and illicit or anorectic drug use. She had previously worked as a waitress. Her mother and her brother had NF-1 but no PH or lung disease.

引用

收藏

页码：E89 / E93

页数：5

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