Moyamoya disease associated with fibromuscular dysplasia of intrapulmonary bronchial arteries-a case report

被引：4

作者：

Stejskal, Vaclav ^{[1
,2
]}

Steiner, Ivo ^{[1
,2
]}

Hornychova, Helena ^{[1
,2
]}

Krupa, Petr ^{[2
,3
]}

Kanta, Martin ^{[2
,3
]}

机构：

[1] Charles Univ Prague, Fac Med, Fingerland Dept Pathol, Hradec Kralove, Czech Republic

[2] Charles Univ Prague, Fac Hosp, Hradec Kralove, Czech Republic

[3] Charles Univ Prague, Dept Neurosurg, Fac Med, Hradec Kralove, Czech Republic

来源：

CARDIOVASCULAR PATHOLOGY | 2020年 / 45卷

关键词：

Moyamoya disease; Bronchial artery; Fibromuscular dysplasia; HYPERTENSION;

D O I：

10.1016/j.carpath.2019.107182

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A case is reported of a 40-year-old woman clinically diagnosed as moyamoya disease with associated fibromuscular dysplasia of intrapulmonary bronchial arteries incidentally revealed during autoptic examination. Moyamoya disease represents an idiopathic noninflammatory and nonatherosclerotic arterio-occlusive process of intracranial arteries. Prolonged brain ischemia leads to formation of tiny and fragile collaterals. Clinically, patients with moyamoya angiopathy commonly present with severe neurological symptoms caused by brain infarction or hemorrhage. Histologically, the steno-occlusive process is based on fibrocellular thickening of intima and intimal smooth muscle cell proliferation. In the literature, extracranial arterial involvement, i.e. fibromuscular dysplasia of renal or pulmonary arteries, has been described in several cases of moyamoya disease. Our aim is to show a unique case of moyamoya disease associated with fibromuscular dysplasia affecting an uncommon site. (C) 2019 Elsevier Inc. All rights reserved.

引用

页数：5

共 19 条

[11] Fibromuscular dysplasia as the substrate for systemic and pulmonary hypertension in the setting of Moya-Moya disease [J].