Parry-Romberg syndrome associated with refractory epilepsy, atrophy of the dura mater and cystic leukoencephalopathy

Case report. We report the clinical and radiologic observation in a man patient of 20 years-old. He developed gravity left progressive facial hemiatrophy. In associated form, he presented numerous visual sensories and complex partials seizures. The single and combined treatment with several antiepileptic drugs was ineffective for the control of the epilepsy. The magnetic resonance investigation of the cranium-facial structures showed the gravity and intensivity of the dysmorphia. The same procedure showed the strong of the duramadre atrophy in the convexity of the brain, as well as, the existence of the cystic formation in the white matter of the left temporo-occipital region at the face affected. Conclusion. We considered, that this is the first report documented fully, about the Parry-Romberg syndrome with refractory epilepsy, duramadre atrophy and cystic leukoencephalopaty, published in Peru.