Currarino triad associated with Hirschsprung's disease

被引：34

作者：

Baltogiannis, N ^{[1
]}

Mavridis, G ^{[1
]}

Soutis, M ^{[1
]}

Keramidas, D ^{[1
]}

机构：

[1] Aghia Sophia Childrens Hosp, Dept Pediat, Athens, Greece

来源：

JOURNAL OF PEDIATRIC SURGERY | 2003年 / 38卷 / 07期

关键词：

Currarino triad; Hirschsprung's disease;

D O I：

10.1016/S0022-3468(03)00199-4

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

The Currarino syndrome is a rare hereditary condition. The major symptom is chronic constipation from early life, and, in more than 80% of the cases, this condition is diagnosed in the first decade. The authors describe an unusual case of a complete Currarino triad associated with Hirschsprung's disease in a 6-year-old girl, presenting persistent constipation and abdominal. distension. The patient is free of symptoms after surgical treatment of anorectal malformation and Hirschsprung's disease. The presacral mass was excised. Complete screening of the pelvis is recommended by using ultrasonography, computed tomography (CT) scan, and radiography in patients with a history of chronic constipation from early childhood. (C) 2003 Elsevier Inc. All rights reserved.

引用

页码：1086 / 1089

页数：4

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