Tailgut cyst (Retrorectal hamartoma):: Report of a pediatric case

被引:14
作者
Galluzzo, M. Laura
Bailez, Marcela
Reusmann, Aixa
Gonzalez, Roberto
de Davila, M. T. G.
机构
[1] Hosp Nacl Pediat, Dept Pathol, Buenos Aires, DF, Argentina
[2] Hosp Nacl Pediat, Dept Surg, Buenos Aires, DF, Argentina
[3] Hosp Nacl Pediat, Dept Neurosurg, Buenos Aires, DF, Argentina
关键词
D O I
10.2350/06-09-0166.1
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Tailgut cyst (TGC) is an uncommon congenital lesion, located in the retrorectal/presacral space. We report a 12-year-old girl with lumbar pain and a retrorectal mass. She had mental retardation, hypothyroidism, didelphus uterus, sacrum vertebrae, and coccyx agenesis, without chromosomic anomalies. Three surgeries were performed for the complete excision of the tumor. Microscopically, the mass consisted of cystic spaces lined by a wide variety of epithelia and a stroma composed of fibrous tissue containing bundles of smooth muscle fibers. According to these findings, the diagnosis was TGC. This is a rare congenital lesion that usually presents as a multiloculated cyst in the retrorectal space of young women; TGC requires complete surgical excision to prevent recurrences, infections, and malignant transformation.. This case was unique because of the association of TGC with other malformative features and concomitant disease in a pediatric patient.
引用
收藏
页码:325 / 327
页数:3
相关论文
共 8 条
[1]   Adenocarcinoma arising in a tailgut cyst with prominent meningothelial proliferation and thyroid tissue: case report and review of the literature [J].
Andea, AA ;
Klimstra, DS .
VIRCHOWS ARCHIV, 2005, 446 (03) :316-321
[2]   TAILGUT CYSTS - REPORT OF 53 CASES [J].
HJERMSTAD, BM ;
HELWIG, EB .
AMERICAN JOURNAL OF CLINICAL PATHOLOGY, 1988, 89 (02) :139-147
[3]   Presacral carcinoid tumors - Report of three cases and review of the literature [J].
Horenstein, MG ;
Erlandson, RA ;
Gonzalez-Cueto, DM ;
Rosai, J .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1998, 22 (02) :251-255
[4]  
Moreira AL, 2001, ARCH PATHOL LAB MED, V125, P1361
[5]  
PIURA B, 2005, ARCH GYNECOL OBSTET, V22, P1
[6]  
Prasad AR, 2000, ARCH PATHOL LAB MED, V124, P725
[7]  
Song DE, 2004, ARCH PATHOL LAB MED, V128, P578
[8]  
Stocker JT, 2002, PEDIAT PATHOLOGY