Carney Complex with Right Ventricular Myxoma following Second Excision of Left Atrial Myxoma

被引:2
作者
Tamura, Yamato [1 ]
Seki, Toshio [1 ]
机构
[1] Nara Prefectural Mimuro Hosp, Dept Cardiovasc Surg, Sango, Nara 6360802, Japan
基金
中国国家自然科学基金;
关键词
Carney complex; myxoma; recurrence; CARDIAC MYXOMAS; RECURRENT; DISEASE;
D O I
10.5761/atcs.cr.13-00058
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report a case of Carney complex with massive right ventricular myxoma after two-time excision of a left atrial myxoma. The patient was a 45-year-old woman with pyrexia. She temporarily lost consciousness during examination, and echocardiography and computed tomography (CT) showed a massive tumor in the right ventricle. Loss of consciousness was determined to be caused by intracardiac obstruction of blood flow due to the tumor, and corrective surgery was performed. Pathological findings indicated myxoma with no malignancy. Myxomas are benign, but there is frequent recurrence of tumors associated with Carney complex. Because her myxomas were accompanied by unusual skin pigmentation, she was diagnosed with Carney complex. Carney complex has a high rate of myxoma recurrence, and often runs in families. In all cases, it is necessary to observe the patient's course closely.
引用
收藏
页码:882 / 884
页数:3
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