Plasma and erythrocyte fatty acid concentrations in long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency

被引:7
|
作者
Lund, AM
Dixon, MA
Vreken, P
Leonard, JV
Morris, AAM
机构
[1] Great Ormond St Hosp Children, Metab Dept, London WC1N 3JH, England
[2] Great Ormond St Hosp Children, Dietet Dept, London WC1N 3JH, England
[3] Univ Amsterdam, Acad Med Ctr, Emma Childrens Hosp, Lab Genet Metab Dis, NL-1105 AZ Amsterdam, Netherlands
关键词
D O I
10.1023/A:1025175606891
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Plasma and erythrocyte fatty acids have been measured in 9 patients with long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency being treated with a low-fat diet. No significant abnormality was detected and in particular docosahexaenoic acid was not deficient.
引用
收藏
页码:410 / 412
页数:3
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