Background: IgG4-related disease (RD) is a recently described fibroinflammatory condition with both cutaneous and systemic manifestations. To our knowledge, the cutaneous manifestations have not been well characterized or systematically investigated to date in the literature. Objective: We sought to describe the cutaneous manifestations of IgG4-RD to guide clinical practice, aid in the diagnosis of IgG4-RD, and contribute to the creation of robust cutaneous diagnostic criteria. Methods: A systematic search of peer-reviewed publications pertaining to cutaneous manifestations of IgG4-RD yielded 56 cases from 32 case reports and series. The clinical findings among the diagnostic categories were compared. Results: Forty cases of IgG4-RD with cutaneous disease were identified. Cutaneous head and neck involvement was significantly associated with a diagnosis of IgG4-RD (P = .02). Macules and bullae were not described in any of the included cases. Among cases of systemic IgG4-RD, cutaneous head and neck involvement was most common and statistically significantly associated with the diagnosis of IgG4-RD(P = .001). Limitations: These findings are limited by reporting and publication bias of particular cases and by small sample size. Conclusions: Papules, plaques, and nodules of the head and neck appear to characterize patients with cutaneous IgG4-RD, which nevertheless usually presents with systemic manifestations.
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Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Hamaguchi, Yasuhito
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Fujimoto, Manabu
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Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Fujimoto, Manabu
;
Matsushita, Yukiyo
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Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Matsushita, Yukiyo
;
Kitamura-Sawada, Seiko
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Kanazawa Univ, Dept Human Pathol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Kitamura-Sawada, Seiko
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Kawano, Mitsuhiro
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Takehara, Kazuhiko
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Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
机构:
ST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USAST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USA
HURT, MA
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CRUZ, DJS
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ST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USAST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USA
机构:
Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Hamaguchi, Yasuhito
;
Fujimoto, Manabu
论文数: 0引用数: 0
h-index: 0
机构:
Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Fujimoto, Manabu
;
Matsushita, Yukiyo
论文数: 0引用数: 0
h-index: 0
机构:
Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Matsushita, Yukiyo
;
Kitamura-Sawada, Seiko
论文数: 0引用数: 0
h-index: 0
机构:
Kanazawa Univ, Dept Human Pathol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
Kitamura-Sawada, Seiko
;
论文数: 引用数:
h-index:
机构:
Kawano, Mitsuhiro
;
Takehara, Kazuhiko
论文数: 0引用数: 0
h-index: 0
机构:
Kanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, JapanKanazawa Univ, Dept Dermatol, Grad Sch Med Sci, Kanazawa, Ishikawa 9208641, Japan
机构:
ST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USAST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USA
HURT, MA
;
CRUZ, DJS
论文数: 0引用数: 0
h-index: 0
机构:
ST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USAST JOHNS MERCY MED CTR, DEPT PATHOL, DIV CUTANEOUS PATHOL, ST LOUIS, MO 63141 USA