Case for diagnosis. Systemic light chain amyloidosis with cutaneous involvement

被引:1
作者
Vianna Gontijo, Joao Renato [1 ]
de Paula, Maysa Carla [1 ]
Pinto, Jackson Machado [1 ]
机构
[1] Santa Casa Belo Horizonte, Dermatol Clin, Belo Horizonte, MG, Brazil
关键词
Amyloidosis; Amyloid; Plaque; amyloid; Ecchymosis; Purpura;
D O I
10.1590/abd1806-4841.20176958
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Systemic light chain amiloydosis is a rare disease. Due to its typical cutaneous lesions, dermatologists play an essential role in its diagnosis. Clinical manifestations vary according to the affected organ and are often unspecific. Definitive diagnosis is achieved through biopsy. We report a patient with palpebral amyloidosis, typical bilateral ecchymoses and cardiac involvement, without plasma cell dyscrasia or lymphomas. The patient died shortly after the diagnosis.
引用
收藏
页码:730 / 731
页数:2
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