Epidermal nevus associated with a type I neurofibromatosis and a nephroblastoma.: A new epidermal nevus syndrome?

被引:0
作者
Courville, P
Thomine, E
Surlemont, Y
Hemet, J
Métayer, J
Lauret, P
机构
[1] CHU Charles Nicolle, Serv Anat Pathol, F-76031 Rouen, France
[2] CHU Charles Nicolle, Dermatol Serv, F-76031 Rouen, France
关键词
epidermal nevus; neurofibromatosis; nephroblastoma;
D O I
暂无
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
We report the case of a 6-year-old boy who showed a large epidermal nevus mixed with a plexiform neurofibroma, which was associated with "cafe au lait" macules and a nephroblastoma. This association could riot be classified in one of the five well defined epidermal nevus syndrome. To our knowledge this is the first tints that this type of epidermal nevus syndrome has been described, which raises the question of the relationship between neurofibromatosis 1, nephroblastoma and epidermal nevus.
引用
收藏
页码:616 / 619
页数:4
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