Erdheim-Chester disease with multisystem involvement in a 4-year-old

被引：18

作者：

Song, Sook Yun ^{[1
]}

Lee, Sun Wha ^{[1
,2
]}

Ryu, Kyung-ha ^{[3
]}

Sung, Sun Hee

机构：

[1] Ewha Womans Univ, Sch Med, Dept Radiol, Seoul, South Korea

[2] Ewha Womans Univ, Mokdong Hosp, Dept Radiol, Seoul 158710, South Korea

[3] Ewha Womans Univ, Sch Med, Dept Pediat, Seoul 158710, South Korea

来源：

PEDIATRIC RADIOLOGY | 2012年 / 42卷 / 05期

关键词：

Erdheim-Chester disease; Histiocytosis; Child; IMAGING FINDINGS; CT;

D O I：

10.1007/s00247-011-2235-8

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Erdheim-Chester disease is a rare form of non-Langerhans histiocytosis of unknown origin occurring mainly in adults. It is extremely rare in children. We report a case of a 4-year-old boy with Erdheim-Chester disease that initially presented as hemifacial palsy and bone pain with multisystem involvement. We describe radiographic findings of bones that show characteristic bilateral symmetrical osteosclerosis with atypical osteolytic lesions in addition to CT findings for pulmonary involvement and MR findings for intracranial lesions.

引用

页码：632 / 635

页数：4

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