PFAPA Syndrome in a Population with Endemic Familial Mediterranean Fever

被引：50
|
作者：
Pehlivan, Esra [1 ]
Adrovic, Amra [1 ]
Sahin, Sezgin [1 ]
Barut, Kenan [1 ]
Cinar, Ovgu Kul [1 ]
Kasapcopur, Ozgur [1 ]
机构：
[1] Istanbul Univ, Cerrahpasa Med Sch, Dept Pediat Rheumatol, Istanbul, Turkey
来源：
JOURNAL OF PEDIATRICS | 2018年 / 192卷
关键词：
PERIODIC FEVER; APHTHOUS STOMATITIS; PHARYNGITIS; TONSILLECTOMY; CHILDREN; COLCHICINE;
D O I：
10.1016/j.jpeds.2017.08.078
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
We reviewed the medical records of patients with periodic fever, aphthosis, pharyngitis, and adenitis (PFAPA) to investigate the clinical course, treatment response, and association with MEFV gene mutation. Familial Mediterranean fever should be considered in patients with PFAPA who do not respond to adenotonsillectomy.
引用
收藏
页码：253 / 255
页数：3
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