Epidermolysis bullosa dystrophica of Hallopeau-Siemens and squamous-cell carcinoma: A case report

被引:11
作者
VanRengen, A
Degreef, H
机构
[1] Department of Dermatology, Katholieke Universiteit Leuven, Universitair Ziekenhuis Sint-Rafael, Leuven
关键词
epidermolysis bullosa dystrophica; squamous-cell carcinoma;
D O I
10.1159/000246438
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A 46-year-old patient suffering from Hallopeau-Siemens type epidermolysis bullosa dystrophica presented a large squamous-cell carcinoma of the left hand. No metastases were observed. The tumour was resected and the phalanxes were amputated. The wound was covered with autologous skin grafts. Squamous-cell carcinoma is extremely aggressive in these patients and surgery is the only effective therapy. This life-threatening complication should always be kept in mind and a biopsy taken of every chronic, non-healing ulceration and of each atypical lesion.
引用
收藏
页码:418 / 420
页数:3
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