Familial Sweet's syndrome in 2 brothers, both seen in the first 2 weeks of life

被引:30
作者
Parsapour, K
Reep, MD
Gohar, K
Shah, V
Church, A
Shwayder, TA
机构
[1] Henry Ford Hosp, Dept Pediat, Detroit, MI 48202 USA
[2] Henry Ford Hosp, Dept Dermatol, Detroit, MI 48202 USA
关键词
D O I
10.1067/mjd.2003.328
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Sweet's syndrome (or acute febrile neutrophilic dermatosis) is a rare inflammatory disease that is characterized by fever, neutrophilia, and painful erythematous plaques that histologically show a dense dermal infiltrate of neutrophils without associated vasculitis. We describe 2 neonates (10 and 15 days of age) with Sweet's syndrome; to our knowledge, this is the first reported case of siblings with Sweet's syndrome.
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页码:132 / 138
页数:7
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