Atrophic dermatofibrosarcoma protuberans: Case report, review, and proposed molecular mechanisms

被引：32

作者：

Young, RJ ^{[1
]}

Albertini, JG

机构：

[1] Wilford Hall USAF Med Ctr, San Antonio, TX 78236 USA

[2] Brooke Army Med Ctr, Dept Dermatol, San Antonio, TX USA

来源：

JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY | 2003年 / 49卷 / 04期

关键词：

D O I：

10.1067/S0190-9622(03)00793-X

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

We report a case of atrophic dermatofibrosarcoma protuberans, an uncommon clinical variant. We discuss molecular and genetic mechanisms of dermatofibrosarcoma protuberans tumorigenesis, review the literature on atrophic dermatofibrosarcoma protuberans, and pose a molecular mechanism for the atrophic variant's phenotype. We also describe using Mohs micrographic excision with CD34 immunostains on the frozen sections to definitively treat the tumor.

引用

收藏

页码：761 / 764

页数：4

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