Patients with acute intermittent porphyria attacks present with severe abdominal pain, neuropathy and psychiatric disturbances. Porphyric neuropathy mostly causes confusion in clinical practice, and patients with porphyria are rarely correctly diagnosed early in the course of the illness. We report a patient with acute intermittent porphyria mimicking Guillain-Barre syndrome with acute onset weakness that rapidly progressed to severe quadriplegia.
机构:
Hop Louis Mourier, Ctr Francais Porphyries, APHP, 178 Rue Renouillers, F-92701 Colombes, France
Univ Paris Diderot, INSERM, U773, Ctr Rech Biomed Bichat Beaujon, Paris, FranceHop Louis Mourier, Ctr Francais Porphyries, APHP, 178 Rue Renouillers, F-92701 Colombes, France
机构:
Hop Louis Mourier, Ctr Francais Porphyries, APHP, 178 Rue Renouillers, F-92701 Colombes, France
Univ Paris Diderot, INSERM, U773, Ctr Rech Biomed Bichat Beaujon, Paris, FranceHop Louis Mourier, Ctr Francais Porphyries, APHP, 178 Rue Renouillers, F-92701 Colombes, France