Response to hydroxyurea among Kuwaiti patients with sickle cell disease and elevated baseline HbF levels

被引:15
作者
Adekile, Adekunle [1 ]
Menzel, Stephan [2 ]
Gupta, Renu [3 ,4 ]
Al-Sharida, Sondus [4 ]
Azab, Asmaa Farag [4 ]
Haider, Mohammad [1 ]
Akbulut, Nagihan [5 ]
Mustafa, Nada [1 ]
Thein, Swee Lay [2 ]
机构
[1] Kuwait Univ, Dept Pediat, Kuwait, Kuwait
[2] Kings Coll London, Fac Life Sci & Med, London WC2R 2LS, England
[3] Kuwait Univ, Dept Radiol, Kuwait, Kuwait
[4] Mubarak Al Kabeer Hosp, Pediat Hematol Unit, Kuwait, Kuwait
[5] Adv Technol Co, Kuwait, Kuwait
关键词
FETAL-HEMOGLOBIN; FEMORAL-HEAD; CHILDREN; ANEMIA;
D O I
10.1002/ajh.24027
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:E138 / E139
页数:2
相关论文
共 6 条
[1]   Hydroxyurea corrects the dysregulated L-selectin expression and increased H2O2 production of polymorphonuclear neutrophils from patients with sickle cell anemia [J].
Benkerrou, M ;
Delarche, C ;
Brahimi, L ;
Fay, M ;
Vilmer, E ;
Elion, J ;
Gougerot-Pocidalo, MA ;
Elbim, C .
BLOOD, 2002, 99 (07) :2297-2303
[2]   Fetal hemoglobin in sickle cell anemia: Genetic studies of the Arab-Indian haplotype [J].
Duyen Ngo ;
Bae, Harold ;
Steinberg, Martin H. ;
Sebastiani, Paola ;
Solovieff, Nadia ;
Baldwin, Clinton T. ;
Melista, Efthymia ;
Safaya, Surinder ;
Farrer, Lindsay A. ;
Al-Suliman, Ahmed M. ;
Albuali, Waleed H. ;
Al Bagshi, Muneer H. ;
Naserullah, Zaki ;
Akinsheye, Idowu ;
Gallagher, Patrick ;
Luo, Hong-yuan ;
Chui, David H. K. ;
Farrell, John J. ;
Al-Ali, Amein K. ;
Alsultan, Abdulrahman .
BLOOD CELLS MOLECULES AND DISEASES, 2013, 51 (01) :22-26
[3]   Fine-mapping at three loci known to affect fetal hemoglobin levels explains additional genetic variation [J].
Galarneau, Genevieve ;
Palmer, Cameron D. ;
Sankaran, Vijay G. ;
Orkin, Stuart H. ;
Hirschhorn, Joel N. ;
Lettre, Guillaume .
NATURE GENETICS, 2010, 42 (12) :1049-1051
[4]   MRI follow-up and natural history of avascular necrosis of the femoral head in Kuwaiti children with sickle cell disease [J].
Gupta, R ;
Adekile, AD .
JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, 2004, 26 (06) :351-353
[5]   Increased prevalence of osteonecrosis of the femoral head in children and adolescents with sickle-cell disease [J].
Mahadeo, Kris M. ;
Oyeku, Suzette ;
Taragin, Benjamin ;
Rajpathak, Swapnil N. ;
Moody, Karen ;
Santizo, Ruth ;
Driscoll, M. Catherine .
AMERICAN JOURNAL OF HEMATOLOGY, 2011, 86 (09) :806-808
[6]   INFLUENCE OF BCL11A, HBS1L-MYB, HBBP1 SINGLE NUCLEOTIDE POLYMORPHISMS AND THE HBG2 XmnI POLYMORPHISM ON Hb F LEVELS [J].
Roy, Papai ;
Bhattacharya, Gargi ;
Mandal, Amrita ;
Dasgupta, Uma B. ;
Banerjee, Debasis ;
Chandra, Sarmila ;
Das, Manikanchan .
HEMOGLOBIN, 2012, 36 (06) :592-599