Absent pulmonary valve syndrome with ascending aortic aneurysm

被引：4
作者：
Liang, Chi-Di [1 ]
Ko, Sheung-Fat [2 ]
Chang, Jen-Ping [3 ]
Huang, Shun-Chen [4 ]
机构：
[1] Chang Gung Univ, Chang Gung Mem Hosp, Dept Pediat, Kaohsiung Med Ctr,Coll Med, Kaohsiung 833, Taiwan
[2] Chang Gung Univ, Chang Gung Mem Hosp, Dept Radiol, Kaohsiung Med Ctr,Coll Med, Kaohsiung, Taiwan
[3] Chang Gung Univ, Chang Gung Mem Hosp, Dept Cardiovasc Surg, Kaohsiung Med Ctr,Coll Med, Kaohsiung, Taiwan
[4] Chang Gung Univ, Chang Gung Mem Hosp, Dept Anat Pathol, Kaohsiung Med Ctr,Coll Med, Kaohsiung, Taiwan
来源：
HEART AND VESSELS | 2010年 / 25卷 / 06期
关键词：
Absent pulmonary valve syndrome; Intact ventricular septum; Pulmonary artery; Ascending aorta; Aneurysm; MARFAN PATIENTS; ROOT; ABNORMALITIES; EXPERIENCE; CHILDREN; DISEASE; ARTERY;
D O I：
10.1007/s00380-010-0014-3
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Absent pulmonary valve syndrome is rare. We report the case of a child with absent pulmonary valve syndrome noted after birth. Progressive dilatation of the main pulmonary artery and ascending aorta were noted by echocardiography and confirmed by heart computed tomography. He underwent ascending aorta graft replacement and pulmonary artery reduction angioplasty at the age of 6. Good outcome was achieved at 18-month follow-up where subsequent computed tomography revealed a normal size ascending aorta and main pulmonary artery.
引用
收藏
页码：569 / 572
页数：4
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