Spontaneous aortic rupture in a patient with neurofibromatosis type 1

被引：7

作者：

Park, Yang Jin ^{[1
]}

Park, Keun Myoung ^{[1
]}

Oh, Jiyoung ^{[2
]}

Park, Hong Suk ^{[2
]}

Kim, Jung-Sun ^{[3
]}

Kim, Young-Wook ^{[1
]}

机构：

[1] Sungkyunkwan Univ, Sch Med, Samsung Med Ctr, Div Vasc Surg,Dept Surg, Seoul 135710, South Korea

[2] Sungkyunkwan Univ, Sch Med, Samsung Med Ctr, Dept Intervent Radiol,Div Vasc Surg, Seoul 135710, South Korea

[3] Sungkyunkwan Univ, Sch Med, Samsung Med Ctr, Dept Pathol,Div Vasc Surg, Seoul 135710, South Korea

来源：

JOURNAL OF THE KOREAN SURGICAL SOCIETY | 2012年 / 82卷 / 04期

关键词：

Aortic aneurysm; Aortic rupture; Neurofibromatosis; 1;

D O I：

10.4174/jkss.2012.82.4.261

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Neurofibromatosis type I (NF-1) is a rare autosomal dominant genetic disorder occurring in 1 in 3,000 individuals. Vasculopathy is a rarely reported finding in patients with NF-1. Here, we report a case of recurrent aortic pseudoaneurysm after endovascular aneurysm repair in a 49-year-old male patient with NF-1. On the sixth postoperative day following a successful open surgical repair of an aortic pseudoaneurysm, he developed hemoperitoneum due to a delayed rupture of the mesenteric artery branch. This was treated with endovascular coil embolization. We report the clinical features and histologic findings of this rare vascular disorder with a review of the relevant literature.

引用

页码：261 / 265

页数：5

共 10 条

[1]

[Anonymous], 1988, Neurofibromatosis, V1, P172

[2] Spontaneous aortic dissection and rupture in a patient with neurofibromatosis [J].