Eosinophilic fasciitis (Shulman's disease): A case series of 11 patients

被引：12

作者：

Naoui, A. ^{[1
]}

Bouslama, K. ^{[1
]}

Abdallah, M. ^{[1
]}

Hamzaoui, S. ^{[1
]}

Arbi, T. ^{[1
]}

Bahri, F. ^{[2
]}

M'zabi, S. ^{[3
]}

Harmel, A. ^{[1
]}

Ennafaa, M. ^{[1
]}

Ben Dridi, M. ^{[1
]}

M'rad, S. ^{[1
]}

机构：

[1] Hop Mongi Slim, Serv Med Interne, La Marsa, Tunisia

[2] Hop Fahat Hached, Serv Med Interne, Sousse, Tunisia

[3] Hap Mongi Slim, Serv Anat Pathol, La Marsa, Tunisia

来源：

REVUE DE MEDECINE INTERNE | 2010年 / 31卷 / 08期

关键词：

Fasciitis; Eosinophilia; Shulman's disease; SYSTEMIC-LUPUS-ERYTHEMATOSUS; DIFFUSE FASCIITIS; THROMBOCYTOPENIC PURPURA; BORRELIA-BURGDORFERI; APLASTIC-ANEMIA; SCLERODERMA; CANCER; CYCLOSPORINE; ANTIBODY; FEATURES;

D O I：

10.1016/j.revmed.2010.03.344

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Purpose. - Eosinophilic fasciitis or Shulman's disease is a rare condition of unknown etiology. Methods. - We report a retrospective case series of 11 patients with eosinophilic fasciitis (seven men and four women, including a single pediatric case) and perform a systematic literature review to determine the main features of this disease. Results. - Mean age of the patients was 46 years. Subcutaneous induration of limbs observed in all the patients was the major presenting symptom. The induration was atypically located in the chest area in two patients. Blood eosinophilia was absent in five cases. Histological fasciitis was demonstrated in all patients and eosinophilic infiltration was present in seven patients. Relapse of subcutaneous induration was observed in only one patient who gradually developed systemic sclerosis. Conclusion. - Diagnosis of eosinophilic fasciitis should be considered in the presence myalgia and subcutaneous induration of limbs, blood eosinophilia and hypergammaglobulinemia. Treatment is based on systemic corticosteroids. (C) 2010 Published by Elsevier Masson SAS on behalf of the Societe nationale francaise de medecine interne (SNFMI).

引用

页码：535 / 539

页数：5

共 61 条

[1] Eosinophilic fasciitis 30 years after - What do we really know? Report of 11 patients and review of the literature [J].