Metanephric stromal tumor: a challenging diagnostic entity in children

被引:6
作者
Kacar, Ayper [1 ]
Azili, Mujdem Nur [2 ]
Cihan, Birsen Songul [3 ]
Demir, Haci Ahmet [4 ]
Tiryaki, Huseyin Tugrul [2 ]
Argani, Pedram [5 ]
机构
[1] Ankara Child Dis Hematol Oncol Training & Res Hos, Dept Pathol, TR-06110 Ankara, Turkey
[2] Ankara Child Dis Hematol Oncol Training & Res Hos, Dept Pediat Surg, TR-06110 Ankara, Turkey
[3] Ankara Child Dis Hematol Oncol Training & Res Hos, Dept Radiol, TR-06110 Ankara, Turkey
[4] Ankara Child Dis Hematol Oncol Training & Res Hos, Dept Oncol, TR-06110 Ankara, Turkey
[5] Johns Hopkins Univ Hosp, Dept Pathol, Baltimore, MD 21287 USA
关键词
Kidney; Metanephric stromal tumor; Pediatric neoplasm; Cyst; PEDIATRIC RENAL NEOPLASM; WILMS-TUMOR; ADENOMA; SPECTRUM;
D O I
10.1016/j.jpedsurg.2011.08.023
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A case with a renal mass diagnosed as metanephric stromal tumor is presented. A 6-year-old boy presented with frequently recurring urinary tract infections. He had been followed up at different medical centers for the last 2 years with a 2 x 2 cm simple cyst localized in the inferior pole of the left kidney. At our center, ultrasonography revealed a heterogeneous mass in the left kidney with a central cystic component. The patient underwent operation for left renal mass, and heminephrectomy was performed. The 5 x 4 x 2.5 cm left heminephrectomy specimen showed a partially cystic mass composed of bland spindle cells distributed haphazardly, entrapping tubules and glomeruli and producing fine collarettes around some tubules. The cysts were lined with a 1-layered flat or cuboidal epithelium. Histopathologically, the tumor was diagnosed as metanephric stromal tumor. Metanephric stromal tumor is a rare renal neoplasm of childhood that can present as a cystic mass, and the solid component can go radiologically undetected because of the blurring infiltrative margins. By presenting this rare entity, the authors suggest that this should be included in the differential diagnosis, thereby helping to avoid complications and unnecessary treatment. (C) 2011 Elsevier Inc. All rights reserved.
引用
收藏
页码:E7 / E10
页数:4
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