Ebstein's anomaly associated with severe valvar pulmonary stenosis: Successful palliation with balloon pulmonary valvuloplasty in an adult

被引:0
作者
Geggel, RL
机构
[1] Childrens Hosp, Dept Cardiol, Boston, MA 02115 USA
[2] Harvard Univ, Sch Med, Dept Pediat, Boston, MA 02115 USA
关键词
congenital heart disease; interventional cardiac catheterization; Ebstein's anomaly; pulmonary stenosis; valvuloplasty;
D O I
10.1002/(SICI)1522-726X(199904)46:4<441::AID-CCD11>3.0.CO;2-7
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report a 52-year-old adult with Ebstein's anomaly associated with severe valvar pulmonary stenosis, secundum atrial septal defect, polycythemia, hypoxemia, and severe exertional limitations. Balloon pulmonary valvuloplasty relieved the valvar obstruction, reduced the degree of tricuspid regurgitation and polycythemia, acid improved systemic oxygenation and exercise abilities. Use of this technique in patients with this combination of lesions can postpone the need for surgical intervention. Cathet. Cardiovasc. Intervent. 46:441-444 1999. (C) 1999 Wiley-Liss, Inc.
引用
收藏
页码:441 / 444
页数:4
相关论文
共 14 条
  • [1] ALIPOUR MS, 1980, JPN HEART J, V21, P883
  • [2] MORBID ANATOMY IN NEONATES WITH EBSTEINS-ANOMALY OF THE TRICUSPID-VALVE - PATHOPHYSIOLOGIC AND CLINICAL IMPLICATIONS
    CELERMAJER, DS
    DODD, SM
    GREENWALD, SE
    WYSE, RKH
    DEANFIELD, JE
    [J]. JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1992, 19 (05) : 1049 - 1053
  • [3] CONGENITALLY CORRECTED TRANSPOSITION AND EBSTEIN ANOMALY OF THE SYSTEMIC ATRIOVENTRICULAR VALVE - ASSOCIATION WITH AORTIC-ARCH OBSTRUCTION
    CELERMAJER, DS
    CULLEN, S
    DEANFIELD, JE
    SULLIVAN, ID
    [J]. JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1991, 18 (04) : 1056 - 1058
  • [4] EBSTEINS-ANOMALY - PRESENTATION AND OUTCOME FROM FETUS TO ADULT
    CELERMAJER, DS
    BULL, C
    TILL, JA
    CULLEN, S
    VASSILLIKOS, VP
    SULLIVAN, ID
    ALLAN, L
    NIHOYANNOPOULOS, P
    SOMERVILLE, J
    DEANFIELD, JE
    [J]. JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1994, 23 (01) : 170 - 176
  • [5] CONGENITAL PULMONIC STENOSIS COMPLICATING EBSTEINS ANOMALY OF TRICUSPID VALVE
    DELEON, AC
    PERLOFF, JK
    BLANCO, P
    [J]. AMERICAN JOURNAL OF CARDIOLOGY, 1964, 14 (05) : 695 - &
  • [6] BALLOON PULMONARY VALVULOPLASTY IN A CHILD WITH EBSTEIN ANOMALY AND VALVAR PULMONARY STENOSIS
    GARRICK, ML
    FISCHER, DR
    ZUBERBUHLER, JR
    [J]. INTERNATIONAL JOURNAL OF CARDIOLOGY, 1989, 23 (02) : 260 - 264
  • [7] PREDICTORS OF LONG-TERM SURVIVAL WITH EBSTEINS-ANOMALY OF THE TRICUSPID-VALVE
    GENTLES, TL
    CALDER, AL
    CLARKSON, PM
    NEUTZE, JM
    [J]. AMERICAN JOURNAL OF CARDIOLOGY, 1992, 69 (04) : 377 - 381
  • [8] TRICUSPID-VALVE DISEASE WITH SIGNIFICANT TRICUSPID INSUFFICIENCY IN THE FETUS - DIAGNOSIS AND OUTCOME
    HORNBERGER, LK
    SAHN, DJ
    KLEINMAN, CS
    COPEL, JA
    REED, KL
    [J]. JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1991, 17 (01) : 167 - 173
  • [9] LEV M, 1970, ARCH PATHOL, V90, P334
  • [10] MAIR DD, 1985, CIRCULATION, V72, P70