Undiagnosed cardiomyopathy in a neonate: significance of low oxygen saturation during anaesthesia

被引:4
作者
Smith, WQ
Abu-Harb, M
机构
[1] Sunderland Royal Hosp, Dept Anaesthesia, Sunderland SR4 7TP, Durham, England
[2] Sunderland Royal Hosp, Dept Neonatol, Sunderland SR4 7TP, England
[3] Sunderland Eye Infirm, Sunderland SR4 7TP, Durham, England
关键词
anaesthesia; paediatric; complications; cardiomyopathy; Sengers syndrome; children;
D O I
10.1093/bja/86.3.435
中图分类号
R614 [麻醉学];
学科分类号
100217 ;
摘要
A case study is described of a 7-day-old full term baby with bilateral congenital cataracts who underwent surgical removal of both cataracts 2 days apart. Problems with oxygen saturation during and after the first anaesthetic prompted further investigation that revealed a nonobstructive hypertrophic cardiomyopathy. The significance and possible causes of low oxygen saturation in a previously healthy neonate during anaesthesia are discussed. The likely diagnosis of Sengers syndrome, and the evaluation of asymptomatic babies with cardiac pathology are discussed.
引用
收藏
页码:435 / 437
页数:3
相关论文
共 14 条
[1]   DEATH IN INFANCY FROM UNRECOGNIZED CONGENITAL HEART-DISEASE [J].
ABUHARB, M ;
HEY, E ;
WREN, C .
ARCHIVES OF DISEASE IN CHILDHOOD, 1994, 71 (01) :3-7
[2]   Prevalence and clinical significance of cardiac murmurs in neonates [J].
Ainsworth, SB ;
Wyllie, JP ;
Wren, C .
ARCHIVES OF DISEASE IN CHILDHOOD-FETAL AND NEONATAL EDITION, 1999, 80 (01) :F43-F45
[3]  
Clarke W R, 1990, J Clin Anesth, V2, P192, DOI 10.1016/0952-8180(90)90097-M
[4]  
COHEN MM, 1990, ANESTH ANALG, V70, P160
[5]  
HICKEY PR, 1985, ANESTH ANALG, V64, P483
[6]   THE NORMAL PULMONARY ARTERIAL PRESSURE DURING THE 1ST YEAR OF LIFE [J].
ROWE, RD ;
JAMES, LS .
JOURNAL OF PEDIATRICS, 1957, 51 (01) :1-4
[7]   CONGENITAL CATARACT AND MITOCHONDRIAL MYOPATHY OF SKELETAL AND HEART-MUSCLE ASSOCIATED WITH LACTIC ACIDOSIS AFTER EXERCISE [J].
SENGERS, RCA ;
HAAR, BGAT ;
TRIJBELS, JMF ;
WILLEMS, JL ;
DANIELS, O ;
STADHOUDERS, AM .
JOURNAL OF PEDIATRICS, 1975, 86 (06) :873-880
[8]  
SENGERS RCA, 1985, BRIT HEART J, V54, P543
[9]  
SKINNER JR, 1997, HEART, V7, P229
[10]   FATAL NEONATAL CARDIOMYOPATHY ASSOCIATED WITH CATARACT AND MITOCHONDRIAL MYOPATHY [J].
SMEITINK, JAM ;
SENGERS, RCA ;
TRIJBELS, JMF ;
RUITENBEEK, W ;
DANIELS, O ;
STADHOUDERS, AM ;
KOCKJANSEN, MJH .
EUROPEAN JOURNAL OF PEDIATRICS, 1989, 148 (07) :656-659