IgG4-related Lung Disease with Organizing Pneumonia Effectively Treated with Azathioprine

被引：6

作者：

Onishi, Yasutaka ^{[1
]}

Kawamura, Tetsuji ^{[1
]}

Kagami, Ryogo ^{[1
]}

Nakahara, Yasuharu ^{[1
]}

Yoshiro, Mochiduki ^{[1
]}

机构：

[1] Natl Hosp Org, Himeji Med Ctr, Dept Resp Med, Himeji, Hyogo, Japan

来源：

INTERNAL MEDICINE | 2014年 / 53卷 / 23期

关键词：

IgG4-related lung disease; IgG4-related pulmonary disease; IgG4-related disease; organizing pneumonia; azathioprine; prednisolone; MULTICENTRIC CASTLEMANS-DISEASE; AUTOIMMUNE PANCREATITIS; SCLEROSING PANCREATITIS; INTERSTITIAL PNEUMONIA; SYSTEMIC-DISEASE; THERAPY; MANIFESTATIONS; EXPERIENCE; CELLS;

D O I：

10.2169/internalmedicine.53.2564

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Immunoglobulin (Ig)-G4-related disease is a multi-organ disease that may affect the lung. We herein describe a patient with IgG4-related lung disease (IgG4-RLD) who was radiologically and pathologically diagnosed with organizing pneumonia. He was successfully treated with a combination of prednisolone (PSL) and azathioprine (AZA), and his clinical course has been uneventful since tapering off PSL. This is a rare case of IgG4-RLD manifesting as organizing pneumonia, and, to our knowledge, this is also the first case showing the effectiveness of AZA in treating IgG4-RLD.

引用

页码：2701 / 2704

页数：4

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