MRI changes in cerebrotendinous xanthomatosis after treatment with chenodeoxycholic acid

被引：1
作者：
Lui, CC
Chang, WN
机构：
[1] Chang Gung Mem Hosp, Dept Neurol, Kaohsiung, Taiwan
[2] Chang Gung Mem Hosp, Dept Diagnost Radiol, Kaohsiung, Taiwan
来源：
RIVISTA DI NEURORADIOLOGIA | 1998年 / 11卷
关键词：
cerebrotendinous xanthomatosis; chenodeoxycholic acid; magnetic resonance imaging;
D O I：
10.1177/19714009980110S203
中图分类号：
Q189 [神经科学];
学科分类号：
071006 ;
摘要：
We report serial changes in MRI findings in three siblings of biochemically and clinically proven cerebrotendinous xanthomatosis (CTX) after treatment with chenodeoxycholic acid (CDCA) 750 mg/day orally for seven years. Clinical and electrophysiological studies are also assessed Electroencephalography (EEG) has improved dramatically whereas the magnetic resonance image(MRI) shows only slight change.
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收藏
页码：8 / 9
页数：2
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