Morbihan disease: a therapeutic challenge

被引：18

作者：

Cabral, Fernanda ^{[1
,2
]}

Lubbe, Lara Caroline ^{[1
,2
]}

Nobrega, Monisa Martins ^{[1
,2
]}

Obadia, Daniel Lago ^{[1
,2
,3
]}

Souto, Roberto ^{[1
,2
]}

Gripp, Alexandre Carlos ^{[1
,2
]}

机构：

[1] Univ Estado Rio De Janeiro, HUPE, Rio De Janeiro, RJ, Brazil

[2] Univ Estado Rio De Janeiro, HUPE, Dermatol Serv, Rio De Janeiro, RJ, Brazil

[3] Univ Estado Rio De Janeiro, HUPE, Serv Dermatopathol, Rio De Janeiro, RJ, Brazil

来源：

ANAIS BRASILEIROS DE DERMATOLOGIA | 2017年 / 92卷 / 06期

关键词：

Glucocorticoids; Isotretinoin; Lymphedema; Rosacea; ROSACEA; LYMPHEDEMA; EDEMA;

D O I：

10.1590/abd1806-4841.20174485

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Morbihan disease is a rare condition characterized by chronic and persistent erythematous solid edema localized on the face. It is believed to be a complication of rosacea and may occur at any stage of the disease. Features of this condition include variable therapeutic response and great refractoriness. We report a case of a 61-year-old man with rosacea history diagnosed with Morbihan disease, who showed excellent therapeutic response with the combination of deflazacort and oral isotretinoin but developed recurrence after corticosteroid discontinuation. We believe that in severe cases of lymphedema of the face this combination is effective and corticosteroid suspension should be done slowly and gradually.

引用

页码：847 / 850

页数：4

共 10 条

[1]

Chen DM, 1997, J AM ACAD DERMATOL, V37, P346

[2]

Erbagci Z, 2000, GAZI MED J, V11, P47

[3] Rosacea lymphoedema of the eyelid [J].